Keratosis Follicularis Spinulosa Decalvans
Keratosis follicularis spinulosa decalvans is a rare X-linked disorder described by Siemens in 1926, a disease that begins in infancy with keratosis pilaris localized on the face, then evolves to more diffuse involvement.: 580, 762 : 649, 714 An association with SAT1 has been suggested.
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